Atypical presentation and management of an epithelioid hemangioma: a case report and review of the literature

Wiggins, Claire J.; Dibbs, Rami P.; Bartlett, Erica L.; Ashton, Daniel J.; Maricevich, Renata S.

doi:10.1186/s43159-020-00064-6

Atypical presentation and management of an epithelioid hemangioma: a case report and review of the literature

Authors

Abstract

Background
Epithelioid hemangioma is a rare, benign vascular lesion classically presenting with painless nodules in the head and neck region. Hemangioma lesions are typically small, located within the dermis and subcutaneous tissue, and rarely exceed 10 cm in size. Complete surgical excision, with negative margins, is the recommended treatment as local recurrence is common. We describe an unusual presentation of epithelioid hemangioma that, to our knowledge, has not been previously described in the literature, epithelioid.
Case presentation
We report an atypical case of a large epithelioid hemangioma lesion with deep intramuscular involvement in a 16-year-old male. Ultrasound and MRI showed a hypervascular mass on the patient’s left upper back, and biopsy confirmed the diagnosis. Treatment consisted of preoperative embolization followed by excision and local tissue rearrangement.
Conclusions
Epithelioid hemangiomas are considered uncommon in the pediatric population. Moreover, it is challenging to diagnose these lesions due to their similarities to other vascular anomalies. We aim to increase awareness of this condition and obtain more precision in diagnosis, thus standardizing the approach for those treating individuals with vascular anomalies.

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